1 Epidermolysis bullosa (EB) - the condition.-

1.1 Definition.-

1.2 Pathology of EB.-

1.2.1 EB simplex (EBS).-

1.2.2 Junctional EB (JEB).-

1.2.3 Dystrophic EB (DEB).-

1.3 The most common sub-types and their signs and symptoms.-

1.4 The most common cutaneous and extra-cutaneous complications.-

1.5 Diagnosis.-

1.6 Therapy.-

2 Motor development in early childhood.-

2.1 Motor development screening.-

2.1.1 Typical development of motor ability.-

2.1.2 Assessment of children with EB.-

2.1.3 Parental questionnaire focusing on the early motor development.-

2.2 Results from motor development screening.-

2.3 Occupational therapy.-

2.3.1 Advising parents.-

2.3.2 OT intervention focusing on the early motor development.-

3 Treatment of the tactile, vestibular and proprioceptive perception.-

3.1 Hypotheses concerning perception.-

3.1.1 The relevance of tactile, vestibular and proprioceptive perception to child development.-

3.2 Assessment of perception.-

3.2.1 Clinical observation of children with EB - considerations.-

3.2.2 Useful additions for children with EB.-

3.3 Assessment results.-

3.3.1 Discussion of the results.-

3.4 Occupational therapy.-

3.4.1 OT intervention focusing on the development of perception.-

4 Development of hand functions.-

4.1 Development of prehension (grasp).-

4.2 Possibilities for assessment of children with EB.-

4.3 Assessment results.-

4.4 Occupational therapy.-

5 Graphomotor skills.-

5.1 Development of pencil grasp and of drawing skills.-

5.2 Assessment of children with EB.-

5.2.1 \'Graphomotorische Testbatterie\'.-

5.2.2 Observation of drawing and writing.-

5.2.3 The \'Mann-Zeichen-Test\'.-

5.3 Assessment results.-

5.4 Occupational therapy.-

5.4.1 OT intervention focusing on drawing and graphomotor skills.-

6 Independence in everyday life and provision of assistive devices.-

6.1 Assessment of children with EB.-

6.1.1 Parental questionnaire focusing on the coping skills of children with EB in everyday life.-

6.2 OT intervention focusing on everyday life and use of assistive devices.-

6.2.1 Self-care.-

6.2.2 Mobility / Locomotion.-

6.2.3 Leisure / Hobbies.-

6.2.4 Kindergarten (nursery) / School / Work.-

6.2.5 Barrier-free living.-

7 Client-directed therapy using the COSA.-

7.1 Client directed practice.-

7.2 What is COSA?.-

7.2.1 Contents and structure of COSA.-

7.3 Client-directed assessment and therapy for children with EB using the COSA.-

7.3.1 Additions to the \'Intended Meaning Reference Guide\' for children with EB.-

7.3.2 Additional items for children with EB.-

7.3.3 Formulating goals.-

8 Rehabilitation of the hand.-

8.1 Pathophysiology of the hand.-

8.2 Contractures and deformities.-

8.2.1 Fingers.-

8.2.2 Thumb.-

8.2.3 Palm and arches of the hand.-

8.2.4 Wrist.-

8.2.5 Interdigital spaces.-

8.2.6 Causes of contractures and their relevance to daily life.-

8.2.7 Pathological changes to the joints due to contractures.-

8.3 Radiological changes.-

8.4 Surgical procedures.-

8.5 Occupational therapy process.-

8.6 Occupational therapy intervention.-

8.7 Occupational therapy assessment.-

8.7.1 Assessment form for the hand - using the AO neutral O-method.-

8.7.2 Assessment form for the hand - range of motion / sensibility / pain / grip forms / dexterity.-

8.7.3 Assessment form for the hand - longitudinal growth und pseudosyndactyly-

8.7.4 Assessment form for the hand - abduction of the digits.-

8.8 Occupational therapy.-

8.8.1 Aims of intervention.-

8.8.2 Bandaging and compression gloves.-

8.8.3 Splinting for contracture prophylaxis.-

8.8.4 Types of splint for contracture prophylaxis.-

8.8.5 Exercises to prevent deformities.-

8.9 Post-operative occupational therapy after digital separation.-

8.9.1 Aims of treatment.-

8.9.2 Post-operative splinting.-

8.9.3